Title :

Cranio-maxillofacial and dental findings in albright's hereditary osteodystrophy and pseudohypoparathyroidism

Author(s) :

Schlund, Matthias [Auteur]
Depeyre, Arnaud [Auteur]
Kohler, Florence [Auteur]
Nicot, Romain [Auteur]
Ferri, Joel [Auteur]
Advanced Drug Delivery Systems (ADDS) - U1008
Médicaments et biomatériaux à libération contrôlée: mécanismes et optimisation - Advanced Drug Delivery Systems - U 1008 [MBLC - ADDS]

Journal title :

The Cleft palate-craniofacial journal . official publication of the American Cleft Palate-Craniofacial Association

Abbreviated title :

Cleft Palate Craniofac. J.

Pages :

1055665618814661

Publication date :

2018-11-29

ISSN :

1545-1569

Keyword(s) :

tooth development
midfacial growth
craniofacial growth
dental anomalies
dental arch
dental occlusion
maxilla
facial morphology
facial growth
craniofacial morphology
tooth agenesis

HAL domain(s) :

Sciences du Vivant [q-bio]

English abstract : [en]

The clinical phenotype of pseudohypoparathyroidism (PHP) is caused by Albright's Hereditary Osteodystrophy (AHO). Often, "round face" the only facial clinical sign reported in the literature. The aim of this study was to ...
Show more >The clinical phenotype of pseudohypoparathyroidism (PHP) is caused by Albright's Hereditary Osteodystrophy (AHO). Often, "round face" the only facial clinical sign reported in the literature. The aim of this study was to highlight various cranio-maxillofacial clinical findings associated with AHO. Four patients presented with PHP type 1a. Only one patient exhibited the classical round face. All patients exhibited dental anomalies, class III malocclusion with maxillary retrusion, and a copper beaten appearance of the skull. One suffered from craniosynostosis. The frequency of craniofacial and dental features associated with malocclusion should prompt careful follow-up, particularly during facial growth, in patients with AHO.Show less >

Language :

Anglais

Audience :

Internationale

Popular science :

Non

Administrative institution(s) :

CHU Lille
Inserm
Université de Lille

Collections :

• Advanced Drug Delivery Systems (ADDS) - U1008

Submission date :

2021-01-20T15:59:14Z